Test Code LAB1409 Amyloidosis, Transthyretin-Associated Familial, Reflex, Blood
Additional Codes
Mayo Test ID |
TTRX |
Performing Laboratory
Mayo Clinic Laboratories in RochesterUseful For
Diagnosis of adult individuals suspected of having transthyretin-associated familial amyloidosis
Testing Algorithm
If familial amyloidosis by liquid chromatography-mass spectrometry is abnormal, DNA sequencing will be performed at an additional charge.
For more information see Amyloidosis (Familial) Test Algorithm.
Special Instructions
Method Name
Affinity Chromatography/Mass Spectrometry (MS)
Reporting Name
Familial Amyloidosis ReflexSpecimen Type
Whole bloodShipping Instructions
Specimen must arrive within 4 days of collection. Specimens are stabilized upon receipt and stored until testing is performed.
Specimen Required
Container/Tube:
Preferred: Lavender top (EDTA)
Acceptable: Yellow top (ACD)
Specimen Volume: 3 mL
Collection Instructions:
1. Invert several times to mix blood.
2. Send whole blood specimen in original tube. Do not aliquot.
Specimen Minimum Volume
0.5 mL
Specimen Stability Information
Specimen Type | Temperature | Time | Special Container |
---|---|---|---|
Whole blood | Refrigerated (preferred) | 4 days | |
Ambient | 4 days |
Reject Due To
Gross hemolysis | OK |
Gross lipemia | OK |
Gross icterus | OK |
Reference Values
An interpretive report will be provided.
Interpretation
The presence of a structural change in transthyretin (TTR) is suggestive of a gene variant that requires confirmation by DNA sequence analysis. A negative result by mass spectrometry does not rule out a TTR variant. Mass spectrometric (MS) results are falsely negative if the amino acid substitution does not produce a measurable mass shift for the transthyretin variant. Approximately 90% of the TTR variants are positive by MS (see Cautions).
After identification of the variant at the DNA level, predictive testing for at-risk family members can be performed by molecular analysis (FMTT / Familial Variant, Targeted Testing, Varies).
Day(s) Performed
Tuesday
Report Available
3 to 9 daysSpecimen Retention Time
2 monthsTest Classification
This test was developed and its performance characteristics determined by Mayo Clinic in a manner consistent with CLIA requirements. It has not been cleared or approved by the US Food and Drug Administration.CPT Code Information
82542
81404 (if appropriate)
LOINC Code Information
Test ID | Test Order Name | Order LOINC Value |
---|---|---|
TTRX | Familial Amyloidosis Reflex | 94864-6 |
Result ID | Test Result Name | Result LOINC Value |
---|---|---|
22668 | Wild Type Mass | 94860-4 |
22669 | Wild Type Width at Half Height | 94863-8 |
22670 | Second Mass | 94862-0 |
22671 | Mass Difference | 94861-2 |
22673 | Abnormal result | 51968-6 |
50944 | Interpretation | 69047-9 |
50946 | Reviewed By | 18771-6 |
Reflex Tests
Test ID | Reporting Name | Available Separately | Always Performed |
---|---|---|---|
TTRZ | TTR Gene, Full Gene Analysis | Yes | No |
Forms
If not ordering electronically, complete, print, and send 1 of the following forms with the specimen: